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D47
Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.0
Mast cell neoplasms of uncertain behavior
  • congenital cutaneous mastocytosis (Q82.2)
  • histiocytic neoplasms of uncertain behavior (D47.Z9)
  • malignant mast cell neoplasm (C96.2-)
D47.01
Cutaneous mastocytosis
  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)
  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa
D47.02
Systemic mastocytosis
  • , if applicable, any associated hematological non-mast cell lineage disease, such as:
  • acute myeloid leukemia (C92.6-, C92.A-)
  • chronic myelomonocytic leukemia (C93.1-)
  • essential thrombocytosis (D47.3)
  • hypereosinophilic syndrome (D72.1)
  • myelodysplastic syndrome (D46.9)
  • myeloproliferative syndrome (D47.1)
  • non-Hodgkin lymphoma (C82-C85)
  • plasma cell myeloma (C90.0-)
  • polycythemia vera (D45)
  • aggressive systemic mastocytosis (C96.21)
  • mast cell leukemia (C94.3-)
  • Indolent systemic mastocytosis
  • Isolated bone marrow mastocytosis
  • Smoldering systemic mastocytosis
  • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
D47.09
Other mast cell neoplasms of uncertain behavior
  • Extracutaneous mastocytoma
  • Mast cell tumor NOS
  • Mastocytoma NOS
  • Mastocytosis NOS
D47.1
Chronic myeloproliferative disease
  • atypical chronic myeloid leukemia BCR/ABL-negative (C92.2-)
  • chronic myeloid leukemia BCR/ABL-positive (C92.1-)
  • myelofibrosis NOS (D75.81)
  • myelophthisic anemia (D61.82)
  • myelophthisis (D61.82)
  • secondary myelofibrosis NOS (D75.81)
  • Chronic neutrophilic leukemia
  • Myeloproliferative disease, unspecified
D47.2
Monoclonal gammopathy
  • Monoclonal gammopathy of undetermined significance [MGUS]
D47.3
Essential (hemorrhagic) thrombocythemia
  • Essential thrombocytosis
  • Idiopathic hemorrhagic thrombocythemia
D47.4
Osteomyelofibrosis
  • acute myelofibrosis (C94.4-)
  • Chronic idiopathic myelofibrosis
  • Myelofibrosis (idiopathic) (with myeloid metaplasia)
  • Myelosclerosis (megakaryocytic) with myeloid metaplasia
  • Secondary myelofibrosis in myeloproliferative disease
D47.Z
Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.Z1
Post-transplant lymphoproliferative disorder (PTLD)
D47.Z2
Castleman disease
  • if applicable human herpesvirus 8 infection (B10.89)
  • Kaposi's sarcoma (C46-)
D47.Z9
Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
  • Histiocytic tumors of uncertain behavior
D47.9
Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified
  • Lymphoproliferative disease NOS