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D56
Thalassemia
D56.0
Alpha thalassemia
  • alpha thalassemia trait or minor (D56.3)
  • asymptomatic alpha thalassemia (D56.3)
  • hydrops fetalis due to isoimmunization (P56.0)
  • hydrops fetalis not due to immune hemolysis (P83.2)
  • Alpha thalassemia major
  • Hemoglobin H Constant Spring
  • Hemoglobin H disease
  • Hydrops fetalis due to alpha thalassemia
  • Severe alpha thalassemia
  • Triple gene defect alpha thalassemia
D56.1
Beta thalassemia
  • beta thalassemia minor (D56.3)
  • beta thalassemia trait (D56.3)
  • delta-beta thalassemia (D56.2)
  • hemoglobin E-beta thalassemia (D56.5)
  • sickle-cell beta thalassemia (D57.4-)
  • Beta thalassemia major
  • Cooley's anemia
  • Homozygous beta thalassemia
  • Severe beta thalassemia
  • Thalassemia intermedia
  • Thalassemia major
D56.2
Delta-beta thalassemia
  • delta-beta thalassemia minor (D56.3)
  • delta-beta thalassemia trait (D56.3)
  • Homozygous delta-beta thalassemia
D56.3
Thalassemia minor
  • alpha thalassemia (D56.0)
  • beta thalassemia (D56.1)
  • delta-beta thalassemia (D56.2)
  • hemoglobin E-beta thalassemia (D56.5)
  • sickle-cell trait (D57.3)
  • Alpha thalassemia minor
  • Alpha thalassemia silent carrier
  • Alpha thalassemia trait
  • Beta thalassemia minor
  • Beta thalassemia trait
  • Delta-beta thalassemia minor
  • Delta-beta thalassemia trait
  • Thalassemia trait NOS
D56.4
Hereditary persistence of fetal hemoglobin [HPFH]
D56.5
Hemoglobin E-beta thalassemia
  • beta thalassemia (D56.1)
  • beta thalassemia minor (D56.3)
  • beta thalassemia trait (D56.3)
  • delta-beta thalassemia (D56.2)
  • delta-beta thalassemia trait (D56.3)
  • hemoglobin E disease (D58.2)
  • other hemoglobinopathies (D58.2)
  • sickle-cell beta thalassemia (D57.4-)
D56.8
Other thalassemias
  • hemoglobin C disease (D58.2)
  • hemoglobin E disease (D58.2)
  • other hemoglobinopathies (D58.2)
  • sickle-cell anemia (D57.-)
  • sickle-cell thalassemia (D57.4)
  • Dominant thalassemia
  • Hemoglobin C thalassemia
  • Mixed thalassemia
  • Thalassemia with other hemoglobinopathy
D56.9
Thalassemia, unspecified
  • Mediterranean anemia (with other hemoglobinopathy)