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D68
Other coagulation defects
D68.0
Von Willebrand's disease
  • capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)
  • Angiohemophilia
  • Factor VIII deficiency with vascular defect
  • Vascular hemophilia
D68.1
Hereditary factor XI deficiency
  • Hemophilia C
  • Plasma thromboplastin antecedent [PTA] deficiency
  • Rosenthal's disease
D68.2
Hereditary deficiency of other clotting factors
  • AC globulin deficiency
  • Congenital afibrinogenemia
  • Deficiency of factor I [fibrinogen]
  • Deficiency of factor II [prothrombin]
  • Deficiency of factor V [labile]
  • Deficiency of factor VII [stable]
  • Deficiency of factor X [Stuart-Prower]
  • Deficiency of factor XII [Hageman]
  • Deficiency of factor XIII [fibrin stabilizing]
  • Dysfibrinogenemia (congenital)
  • Hypoproconvertinemia
  • Owren's disease
  • Proaccelerin deficiency
D68.3
Hemorrhagic disorder due to circulating anticoagulants
D68.31
Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.311
Acquired hemophilia
  • Autoimmune hemophilia
  • Autoimmune inhibitors to clotting factors
  • Secondary hemophilia
D68.312
Antiphospholipid antibody with hemorrhagic disorder
  • antiphospholipid antibody, finding without diagnosis (R76.0)
  • antiphospholipid antibody syndrome (D68.61)
  • antiphospholipid antibody with hypercoagulable state (D68.61)
  • lupus anticoagulant (LAC) finding without diagnosis (R76.0)
  • lupus anticoagulant (LAC) with hypercoagulable state (D68.62)
  • systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
  • systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.62)
  • Lupus anticoagulant (LAC) with hemorrhagic disorder
  • Systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder
D68.318
Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
  • Antithromboplastinemia
  • Antithromboplastinogenemia
  • Hemorrhagic disorder due to intrinsic increase in antithrombin
  • Hemorrhagic disorder due to intrinsic increase in anti-VIIIa
  • Hemorrhagic disorder due to intrinsic increase in anti-IXa
  • Hemorrhagic disorder due to intrinsic increase in anti-XIa
D68.32
Hemorrhagic disorder due to extrinsic circulating anticoagulants
  • Drug-induced hemorrhagic disorder
  • Hemorrhagic disorder due to increase in anti-IIa
  • Hemorrhagic disorder due to increase in anti-Xa
  • Hyperheparinemia
D68.4
Acquired coagulation factor deficiency
  • vitamin K deficiency of newborn (P53)
  • Deficiency of coagulation factor due to liver disease
  • Deficiency of coagulation factor due to vitamin K deficiency
D68.5
Primary thrombophilia
  • antiphospholipid syndrome (D68.61)
  • lupus anticoagulant (D68.62)
  • secondary activated protein C resistance (D68.69)
  • secondary antiphospholipid antibody syndrome (D68.69)
  • secondary lupus anticoagulant with hypercoagulable state (D68.69)
  • secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)
  • systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
  • systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)
  • thrombotic thrombocytopenic purpura (M31.1)
  • Primary hypercoagulable states
D68.51
Activated protein C resistance
  • Factor V Leiden mutation
D68.52
Prothrombin gene mutation
D68.59
Other primary thrombophilia
  • Antithrombin III deficiency
  • Hypercoagulable state NOS
  • Primary hypercoagulable state NEC
  • Primary thrombophilia NEC
  • Protein C deficiency
  • Protein S deficiency
  • Thrombophilia NOS
D68.6
Other thrombophilia
  • diffuse or disseminated intravascular coagulation [DIC] (D65)
  • heparin induced thrombocytopenia (HIT) (D75.82)
  • hyperhomocysteinemia (E72.11)
  • Other hypercoagulable states
D68.61
Antiphospholipid syndrome
  • anti-phospholipid antibody, finding without diagnosis (R76.0)
  • anti-phospholipid antibody with hemorrhagic disorder (D68.312)
  • lupus anticoagulant syndrome (D68.62)
  • Anticardiolipin syndrome
  • Antiphospholipid antibody syndrome
D68.62
Lupus anticoagulant syndrome
  • anticardiolipin syndrome (D68.61)
  • antiphospholipid syndrome (D68.61)
  • lupus anticoagulant (LAC) finding without diagnosis (R76.0)
  • lupus anticoagulant (LAC) with hemorrhagic disorder (D68.312)
  • Lupus anticoagulant
  • Presence of systemic lupus erythematosus [SLE] inhibitor
D68.69
Other thrombophilia
  • Hypercoagulable states NEC
  • Secondary hypercoagulable state NOS
D68.8
Other specified coagulation defects
  • hemorrhagic disease of newborn (P53)
D68.9
Coagulation defect, unspecified