Alphabetic Index | Tabular List | Neoplasms | Drugs and Chemicals | Injuries
D81
Combined immunodeficiencies
D81.0
Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3
Adenosine deaminase [ADA] deficiency
D81.4
Nezelof's syndrome
D81.5
Purine nucleoside phosphorylase [PNP] deficiency
D81.6
Major histocompatibility complex class I deficiency
  • Bare lymphocyte syndrome
D81.7
Major histocompatibility complex class II deficiency
D81.8
Other combined immunodeficiencies
D81.81
Biotin-dependent carboxylase deficiency
  • biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
  • Multiple carboxylase deficiency
D81.810
Biotinidase deficiency
D81.818
Other biotin-dependent carboxylase deficiency
  • Holocarboxylase synthetase deficiency
  • Other multiple carboxylase deficiency
D81.819
Biotin-dependent carboxylase deficiency, unspecified
  • Multiple carboxylase deficiency, unspecified
D81.89
Other combined immunodeficiencies
D81.9
Combined immunodeficiency, unspecified
  • Severe combined immunodeficiency disorder [SCID] NOS