D89

Other disorders involving the immune mechanism, not elsewhere classified

hyperglobulinemia NOS (R77.1)
monoclonal gammopathy (of undetermined significance) (D47.2)

transplant failure and rejection (T86.-)

D89.0

Polyclonal hypergammaglobulinemia

Benign hypergammaglobulinemic purpura
Polyclonal gammopathy NOS

D89.1

Cryoglobulinemia

Cryoglobulinemic purpura
Cryoglobulinemic vasculitis
Essential cryoglobulinemia
Idiopathic cryoglobulinemia
Mixed cryoglobulinemia
Primary cryoglobulinemia
Secondary cryoglobulinemia

D89.2

Hypergammaglobulinemia, unspecified

D89.3

Immune reconstitution syndrome

Immune reconstitution inflammatory syndrome [IRIS]

D89.4

Mast cell activation syndrome and related disorders

aggressive systemic mastocytosis (C96.21)
congenital cutaneous mastocytosis (Q82.2)
(non-congenital) cutaneous mastocytosis (D47.01)
(indolent) systemic mastocytosis (D47.02)
malignant mast cell neoplasm (C96.2-)
malignant mastocytoma (C96.29)
mast cell leukemia (C94.3-)
mast cell sarcoma (C96.22)
mastocytoma NOS (D47.09)
other mast cell neoplasms of uncertain behavior (D47.09)
systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)

D89.40

Mast cell activation, unspecified

Mast cell activation disorder, unspecified
Mast cell activation syndrome, NOS

D89.41

Monoclonal mast cell activation syndrome

D89.42

Idiopathic mast cell activation syndrome

D89.43

Secondary mast cell activation

underlying etiology, if known

Secondary mast cell activation syndrome

D89.49

Other mast cell activation disorder

Other mast cell activation syndrome

D89.8

Other specified disorders involving the immune mechanism, not elsewhere classified

D89.81

Graft-versus-host disease

D89.810

Acute graft-versus-host disease

D89.811

Chronic graft-versus-host disease

D89.812

Acute on chronic graft-versus-host disease

D89.813

Graft-versus-host disease, unspecified

D89.82

Autoimmune lymphoproliferative syndrome [ALPS]

D89.89

Other specified disorders involving the immune mechanism, not elsewhere classified

human immunodeficiency virus disease (B20)

D89.9

Disorder involving the immune mechanism, unspecified

Immune disease NOS