E74

Other disorders of carbohydrate metabolism

diabetes mellitus (E08-E13)
hypoglycemia NOS (E16.2)
increased secretion of glucagon (E16.3)
mucopolysaccharidosis (E76.0-E76.3)

E74.0

Glycogen storage disease

E74.00

Glycogen storage disease, unspecified

E74.01

von Gierke disease

Type I glycogen storage disease

E74.02

Pompe disease

Cardiac glycogenosis
Type II glycogen storage disease

E74.03

Cori disease

Forbes disease
Type III glycogen storage disease

E74.04

McArdle disease

Type V glycogen storage disease

E74.09

Other glycogen storage disease

Andersen disease
Hers disease
Tauri disease
Glycogen storage disease, types 0, IV, VI-XI
Liver phosphorylase deficiency
Muscle phosphofructokinase deficiency

E74.1

Disorders of fructose metabolism

muscle phosphofructokinase deficiency (E74.09)

E74.10

Disorder of fructose metabolism, unspecified

E74.11

Essential fructosuria

Fructokinase deficiency

E74.12

Hereditary fructose intolerance

Fructosemia

E74.19

Other disorders of fructose metabolism

Fructose-1, 6-diphosphatase deficiency

E74.2

Disorders of galactose metabolism

E74.20

Disorders of galactose metabolism, unspecified

E74.21

Galactosemia

E74.29

Other disorders of galactose metabolism

Galactokinase deficiency

E74.3

Other disorders of intestinal carbohydrate absorption

lactose intolerance (E73.-)

E74.31

Sucrase-isomaltase deficiency

E74.39

Other disorders of intestinal carbohydrate absorption

Disorder of intestinal carbohydrate absorption NOS
Glucose-galactose malabsorption
Sucrase deficiency

E74.4

Disorders of pyruvate metabolism and gluconeogenesis

disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
Leigh's syndrome (G31.82)

Deficiency of phosphoenolpyruvate carboxykinase
Deficiency of pyruvate carboxylase
Deficiency of pyruvate dehydrogenase

E74.8

Other specified disorders of carbohydrate metabolism

Essential pentosuria
Renal glycosuria

E74.9

Disorder of carbohydrate metabolism, unspecified