Alphabetic Index | Tabular List | Neoplasms | Drugs and Chemicals | Injuries
E76
Disorders of glycosaminoglycan metabolism
E76.0
Mucopolysaccharidosis, type I
E76.01
Hurler's syndrome
E76.02
Hurler-Scheie syndrome
E76.03
Scheie's syndrome
E76.1
Mucopolysaccharidosis, type II
  • Hunter's syndrome
E76.2
Other mucopolysaccharidoses
E76.21
Morquio mucopolysaccharidoses
E76.210
Morquio A mucopolysaccharidoses
  • Classic Morquio syndrome
  • Morquio syndrome A
  • Mucopolysaccharidosis, type IVA
E76.211
Morquio B mucopolysaccharidoses
  • Morquio-like mucopolysaccharidoses
  • Morquio-like syndrome
  • Morquio syndrome B
  • Mucopolysaccharidosis, type IVB
E76.219
Morquio mucopolysaccharidoses, unspecified
  • Morquio syndrome
  • Mucopolysaccharidosis, type IV
E76.22
Sanfilippo mucopolysaccharidoses
  • Mucopolysaccharidosis, type III (A) (B) (C) (D)
  • Sanfilippo A syndrome
  • Sanfilippo B syndrome
  • Sanfilippo C syndrome
  • Sanfilippo D syndrome
E76.29
Other mucopolysaccharidoses
  • beta-Glucuronidase deficiency
  • Maroteaux-Lamy (mild) (severe) syndrome
  • Mucopolysaccharidosis, types VI, VII
E76.3
Mucopolysaccharidosis, unspecified
E76.8
Other disorders of glucosaminoglycan metabolism
E76.9
Glucosaminoglycan metabolism disorder, unspecified