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E77
Disorders of glycoprotein metabolism
E77.0
Defects in post-translational modification of lysosomal enzymes
  • Mucolipidosis II [I-cell disease]
  • Mucolipidosis III [pseudo-Hurler polydystrophy]
E77.1
Defects in glycoprotein degradation
  • Aspartylglucosaminuria
  • Fucosidosis
  • Mannosidosis
  • Sialidosis [mucolipidosis I]
E77.8
Other disorders of glycoprotein metabolism
E77.9
Disorder of glycoprotein metabolism, unspecified