Alphabetic Index | Tabular List | Neoplasms | Drugs and Chemicals | Injuries
M04
Autoinflammatory syndromes
M04.1
Periodic fever syndromes
  • Familial Mediterranean fever
  • Hyperimmunoglobin D syndrome
  • Mevalonate kinase deficiency
  • Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
M04.2
Cryopyrin-associated periodic syndromes
  • Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
  • Familial cold autoinflammatory syndrome
  • Familial cold urticaria
  • Muckle-Wells syndrome
  • Neonatal onset multisystemic inflammatory disorder [NOMID]
M04.8
Other autoinflammatory syndromes
  • Blau syndrome
  • Deficiency of interleukin 1 receptor antagonist [DIRA]
  • Majeed syndrome
  • Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
  • Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]
M04.9
Autoinflammatory syndrome, unspecified