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Q89
Other congenital malformations, not elsewhere classified
Q89.0
Congenital absence and malformations of spleen
  • isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)
Q89.01
Asplenia (congenital)
Q89.09
Congenital malformations of spleen
  • Congenital splenomegaly
Q89.1
Congenital malformations of adrenal gland
  • adrenogenital disorders (E25.-)
  • congenital adrenal hyperplasia (E25.0)
Q89.2
Congenital malformations of other endocrine glands
  • congenital goiter (E03.0)
  • congenital hypothyroidism (E03.1)
  • Congenital malformation of parathyroid or thyroid gland
  • Persistent thyroglossal duct
  • Thyroglossal cyst
Q89.3
Situs inversus
  • dextrocardia NOS (Q24.0)
  • Dextrocardia with situs inversus
  • Mirror-image atrial arrangement with situs inversus
  • Situs inversus or transversus abdominalis
  • Situs inversus or transversus thoracis
  • Transposition of abdominal viscera
  • Transposition of thoracic viscera
Q89.4
Conjoined twins
  • Craniopagus
  • Dicephaly
  • Pygopagus
  • Thoracopagus
Q89.7
Multiple congenital malformations, not elsewhere classified
  • congenital malformation syndromes affecting multiple systems (Q87.-)
  • Multiple congenital anomalies NOS
  • Multiple congenital deformities NOS
Q89.8
Other specified congenital malformations
Q89.9
Congenital malformation, unspecified
  • Congenital anomaly NOS
  • Congenital deformity NOS